吃奶呻吟打开双腿做受动态图 -亚洲色偷偷色噜噜狠狠99网-日韩精品极品视频在线观看免费-来一水AV@lysav

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  人才招聘  關(guān)于我們  聯(lián)系我們
亚洲欧美日本韩国,精品欧美一区二区三区久久久
Rabbit Anti-Bestrophin/RBITC Conjugated antibody (bs-11040R-RBITC)
訂購(gòu)熱線:400-901-9800
訂購(gòu)郵箱:sales@xucheq.com
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@xucheq.com
說(shuō) 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-11040R-RBITC
英文名稱1 Rabbit Anti-Bestrophin/RBITC Conjugated antibody
中文名稱 羅丹明(RBITC)標(biāo)記的卵黃狀黃斑病蛋白抗體
別    名 BEST 1; BEST1; BEST-1; BEST; Best macular dystrophy; BEST1; BEST1_HUMAN; Bestrophin 1; Bestrophin-1; Bestrophin1; BMD; mBest1; TU15B; Vitelliform macular dystrophy 2; Vitelliform macular dystrophy; Vitelliform macular dystrophy protein 2; VMD 2; VMD2.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買        大包裝/詢價(jià)
說(shuō) 明 書 100ul  
研究領(lǐng)域 神經(jīng)生物學(xué)  細(xì)胞粘附分子  
抗體來(lái)源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 64kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Bestrophin
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Best vitelliform macular dystrophy, known as Best disease, is an early-onset autosomal dominant condition in which accumulation of lipofuscin-like material within and beneath the RPE leads to progressive loss of central vision. Best disease is frequently a reflection of mutations in the Bestrophin gene, which encodes a protein containing four putative transmembrane domains and localizes to the basolateral plasma membrane of RPE cells. Human Bestrophin forms oligomeric chloride channels that are sensitive to intracellular calcium. Missense mutations at the Bestrophin locus reduces or abolishes Bestrophin protein mediated membrane current. Bestrophin Bestrophin 2,Bestrophin 3, and Bestrophin 4 are transmembrane proteins that contain a high percentage of aromatic residues, a conserved RFP (Arg-Phe-Pro) motif and they function as anion channels.

Function:
Forms calcium-sensitive chloride channels. Highly permeable to bicarbonate.

Subunit:
Tetramer or pentamers. May interact with PPP2CB and PPP2R1B.

Subcellular Location:
Cell membrane. Basolateral cell membrane.

Tissue Specificity:
Predominantly expressed in the basolateral membrane of the retinal pigment epithelium.

Post-translational modifications:
Phosphorylated by PP2A.

DISEASE:
Defects in BEST1 are the cause of vitelliform macular dystrophy type 2 (VMD2) ; also known as Best macular dystrophy (BMD). VMD2 is an autosomal dominant form of macular degeneration that usually begins in childhood or adolescence. VMD2 is characterized by typical 'egg-yolk' macular lesions due to abnormal accumulation of lipofuscin within and beneath the retinal pigment epithelium cells. Progression of the disease leads to destruction of the retinal pigment epithelium and vision loss.
Defects in BEST1 are the cause of retinitis pigmentosa type 50 (RP50) . A retinal dystrophy belonging to the group of pigmentary retinopathies. RP is characterized by retinal pigment deposits visible on fundus examination and primary loss of rod photoreceptor cells followed by secondary loss of cone photoreceptors. Patients typically have night vision blindness and loss of midperipheral visual field. As their condition progresses, they lose their far peripheral visual field and eventually central vision as well.

Similarity:
Belongs to the bestrophin family.

Database links:

Entrez Gene: 7439 Human

Entrez Gene: 24115 Mouse

Entrez Gene: 293735 Rat

Omim: 607854 Human

SwissProt: O76090 Human

SwissProt: O88870 Mouse

Unigene: 524910 Human

Unigene: 712676 Human

Unigene: 31577 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.xucheq.com 北京博奧森生物技術(shù)有限公司
通過(guò)國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過(guò)國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
免费A级毛片无码| CHINESE熟女熟妇1乱| 亚洲 精品 综合 精品 自拍| 肥老熟妇伦子伦456视频| 麻豆妓女爽爽一区二区三| 国产特黄A片AAAA毛片| 再深点灬舒服灬受不了了视频| 爱的色放在线播放| 国产成人亚洲精品无码AV大片| 国模无码一区二区三区| 日本乱偷中文字幕| 无套内谢的新婚少妇国语播放| 久久精品夜色噜噜亚洲A∨| CHINESE老女人老熟妇HD| 无码AV中文一区二区三区桃花岛| 国产午夜福利视频在线观看| 无码人妻久久一区二区三区免费丨| 朋友的妈妈在线观看| 午夜精品久久久久久| 色综合久久久无码中文字幕波多| 欧洲-级毛片内射| 破了亲妺妺的处免费视频国产| 国产精品久久人妻互换| 波多野结衣绝顶大高潮| 亚洲AV无码成人黄网站在线观看 | 被C哭着爬走又被拉回来挺进H| 亚洲第一综合天堂另类专| 大陆熟妇丰满多毛XXXX| 精品无码国产一区二区三区麻豆| 免费观看黄色电影| 国产裸拍裸体视频在线观看| 搡BBBB搡BBB搡| 人色偷偷色AV噜噜狠狠99| 中文字幕被公侵犯的漂亮人妻| 成人免费ā片在线观看| 少妇性按摩无码中文A片| 精品人体无码一区二区三区| 亚洲AV无码一区二区一二区| 色偷偷88888欧美精品久久久 | 中国人妻被两个老外三P| 97SE亚洲国产综合在线|