吃奶呻吟打开双腿做受动态图 -亚洲色偷偷色噜噜狠狠99网-日韩精品极品视频在线观看免费-来一水AV@lysav

掃碼關(guān)注公眾號(hào)           掃碼咨詢(xún)技術(shù)支持           掃碼咨詢(xún)技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  人才招聘  關(guān)于我們  聯(lián)系我們
51精产一二三产区区别,CHINESE熟女老女人HD,国产伦精品一区二区三区妓女
Rabbit Anti-CLCN2/PE Conjugated antibody (bs-6470R-PE)
訂購(gòu)熱線:400-901-9800
訂購(gòu)郵箱:sales@xucheq.com
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@xucheq.com
說(shuō) 明 書(shū): 100ul  
100ul/2980.00元
大包裝/詢(xún)價(jià)
產(chǎn)品編號(hào) bs-6470R-PE
英文名稱(chēng)1 Rabbit Anti-CLCN2/PE Conjugated antibody
中文名稱(chēng) PE標(biāo)記的氯離子通道蛋白2抗體
別    名 Chloride Channel 2; Chloride channel protein 2; Chloride channel, voltage sensitive 2; CIC 2; CIC2; ClC-2; CLC2; Clcn2; CLCN2_HUMAN; ECA2; ECA3; EG13; EGI11; EGMA; EJM6; EJM8.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買(mǎi)        大包裝/詢(xún)價(jià)
說(shuō) 明 書(shū) 100ul  
研究領(lǐng)域 細(xì)胞生物  神經(jīng)生物學(xué)  信號(hào)轉(zhuǎn)導(dǎo)  通道蛋白  
抗體來(lái)源 Rabbit
克隆類(lèi)型 Polyclonal
交叉反應(yīng) Human,  (predicted: Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, .)
產(chǎn)品應(yīng)用 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 99kDa
細(xì)胞定位 細(xì)胞膜 
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human CLCN2/CLC-2
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
The family of voltage-dependent chloride channels (CLCs) regulate cellular trafficking of chloride ions, a critical component of all living cells. CLCs regulate excitability in muscle and nerve cells, aid in organic solute transport and maintain cellular volume. The genes encoding human CLC-1 through CLC-7 map to chromosomes 7q32, 3q28, 4q32, Xp22.3, Xp11.23-p11.22, 1p36 and 16p13, respectively. CLC1 is highly expressed in skeletal muscle. Mutations in the gene encoding CLC1 lead to myotonia, an inheritable disorder characterized by muscle stiffness and renal salt wasting. CLC2 is highly expressed in the epithelia of several organs including lung, which suggests CLC2 may be a possible therapeutic target for cystic fibrosis. CLC3 expression is particularly abundant in neuronal tissue, while CLC4 expression is evident in skeletal and cardiac muscle as well as brain. Mutations in the gene encoding CLC5 lead to Dent’s disease, a renal disorder characterized by proteinuria and hypercalciuria. CLC6 and CLC7 are broadly expressed in several tissues including testis, kidney, brain and muscle.

Function:
Voltage-gated chloride channel. Chloride channels have several functions including the regulation of cell volume; membrane potential stabilization, signal transduction and transepithelial transport.

Subcellular Location:
Membrane; Multi-pass membrane protein.

Tissue Specificity:
Ubiquitously expressed. Moderately expressed in aortic and coronary vascular smooth muscle cells and expressed at a low level in aortic endothelial cells.

DISEASE:
Defects in CLCN2 are associated with susceptibility to epilepsy, idiopathic generalized type 11 (EIG11) [MIM:607628]. A disorder characterized by recurring generalized seizures in the absence of detectable brain lesions and/or metabolic abnormalities. Generalized seizures arise diffusely and simultaneously from both hemispheres of the brain.
Defects in CLCN2 are associated with juvenile absence epilepsy type 2 (JAE2) [MIM:607628]. JAE is a subtype of idiopathic generalized epilepsy (IGE) characterized by onset occurring around puberty, absence seizures, generalized tonic-clonic seizures (GTCS), GTCS on awakening and myoclonic seizures.
Defects in CLCN2 are associated with juvenile myoclonic epilepsy type 8 (EJM8) [MIM:607628]. A subtype of idiopathic generalized epilepsy. Patients have afebrile seizures only, with onset in adolescence (rather than in childhood) and myoclonic jerks which usually occur after awakening and are triggered by sleep deprivation and fatigue.

Similarity:
Belongs to the chloride channel (TC 2.A.49) family. ClC-2/CLCN2 subfamily.
Contains 2 CBS domains.

Database links:

Entrez Gene: 1181 Human

Entrez Gene: 12724 Mouse

Entrez Gene: 29232 Rat

Omim: 600570 Human

SwissProt: P51788 Human

SwissProt: Q6IPA9 Human

SwissProt: Q9R0A1 Mouse

SwissProt: P35525 Rat

Unigene: 436847 Human

Unigene: 177761 Mouse

Unigene: 11073 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.xucheq.com 北京博奧森生物技術(shù)有限公司
通過(guò)國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書(shū)編號(hào): 00124Q34771R2M/1100
通過(guò)國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書(shū)編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
夜月直播视频直播免费观看| 亚洲AV无码一区二区三区人| 中文字幕AV久久一区二区| 成全动漫视频在线观看免费高清 | 国产精品久久久| 亚洲AV无码一区二区二三区入口| 免费国偷自产拍精品视频| 国产AV一区二区三区日韩| 免费看又黄又无码的网站| 精品无码一区二区三区| 处破女轻点疼丨98分钟| 狠狠色噜噜狠狠狠狠色综合久 | 老熟妇仑乱视频一区二区| 被黑人猛躁10次高潮视频 | 真实的国产乱XXXX在线| 成人性爱视频在线观看| ASS白嫩白嫩的少妇PICS| 精品人妻无码一区二区三区淑枝| 老BWBWBWBWBWBWBW| 18禁白丝喷水视频WWW视频| 农村熟女XXXXHD做受| 天天爽夜夜爽夜夜爽精品视频 | 天天爽夜夜爽夜夜爽精品视频| 无码欧精品亚洲日韩一区| 少妇荡乳情欲办公室456视频 | 国产成人精品久久| 久久中文字幕人妻熟AV女| 99久久久无码国产精品不卡| 免费60分钟床| 国产精品无码专区| 成人AAA片一区国产精品| 国产人妻777人伦精品HD| 日本特黄特色AAA大片免费| 国产成人午夜精品久久久久久| 女厕偷窥一区二区三区| 亚洲日韩精品欧美一区二区一| 久久久久亚洲AV成人无码电影| 亚洲乱码日产精品BD在线观看| 天天做夜夜躁狠狠躁视频| 国产麻豆一精品一AV一免费| 亚洲精品中文字幕乱码三区 |