吃奶呻吟打开双腿做受动态图 -亚洲色偷偷色噜噜狠狠99网-日韩精品极品视频在线观看免费-来一水AV@lysav

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  人才招聘  關(guān)于我們  聯(lián)系我們
亚洲精品乱码久久久久久蜜桃图片 ,久久久噜噜噜久久中文字幕色伊伊
Rabbit Anti-KCTD7/Cy7 Conjugated antibody (bs-11729R-Cy7)
訂購(gòu)熱線:400-901-9800
訂購(gòu)郵箱:sales@xucheq.com
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@xucheq.com
說(shuō) 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-11729R-Cy7
英文名稱1 Rabbit Anti-KCTD7/Cy7 Conjugated antibody
中文名稱 Cy7標(biāo)記的鉀離子通道多聚體結(jié)構(gòu)域蛋白7抗體
別    名 BTB/POZ domain containing protein KCTD7; EPM3; FLJ32069; Potassium channel tetramerisation domain containing 7; KCTD7_HUMAN.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買        大包裝/詢價(jià)
說(shuō) 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  神經(jīng)生物學(xué)  通道蛋白  細(xì)胞膜受體  
抗體來(lái)源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep, )
產(chǎn)品應(yīng)用
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 33kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human KCTD7 (112-180aa)
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Epilepsy affects about 0.5% of the world’s population and has a large genetic component. Epilepsy results from an electrical hyperexcitability in the central nervous system. Potassium channels are important regulators of electrical signaling, determining the firing properties and responsiveness of a variety of neurons. Benign familial neonatal convulsions (BFNC), an autosomal dominant epilepsy of infancy, has been shown to be caused by mutations in the KCNQ2 or the KCNQ3 potassium channel genes. KCNQ2 and KCNQ3 are voltage-gated potassium channel proteins with six putative transmembrane domains. Both proteins display a broad distribution within the brain, with expression patterns that largely overlap.

Function:
The KCTD gene family, including KCTD7, encode predicted proteins that contain N terminal domain that is homologous to the T1 domain in voltage gated potassium channels. KCTD7 displays a primary sequence and hydropathy profile indicating intracytoplasmic localization. There are two named isoforms.

Subunit:
May be involved in the control of excitability of cortical neurons

Subcellular Location:
Cell membrane. Cytoplasm, cytosol.

DISEASE:
efects in KCTD7 are the cause of epilepsy, progressive myoclonic 3, with or without intracellular inclusions (EPM3) [MIM:611726]. EPM3 is an autosomal recessive, severe, progressive myoclonic epilepsy with early-onset. Multifocal myoclonic seizures begin between 16 and 24 months of age after normal initial development. Neurodegeneration and regression occur with seizure onset. Other features include mental retardation, dysarthria, truncal ataxia, and loss of fine finger movements. EEG shows slow dysrhythmia, multifocal and occasionally generalized epileptiform discharges. In some patients, ultrastructural findings on skin biopsies identify intracellular accumulation of autofluorescent lipopigment storage material, consistent with neuronal ceroid lipofuscinosis.
Note=Defects in KCTD7 are a cause of opsoclonus-myoclonus ataxia-like syndrome. Opsoclonus myoclonus ataxia syndrome (OMS) is a rare pervasive and frequently permanent disorder that usually develops in previously healthy children with normal premorbid psychomotor development and characterized by association of abnormal eye movements (opsoclonus), severe dyskinesia (myoclonus), cerebellar ataxia, functional regression, and behavioral problems. The syndrome is considered to be an immune-mediated disorder and may be tumor-associated or idiopathic. OMS is one of a few steroid responsive disorders of childhood. KCTD7 mutations have been found in a patient with an atypical clinical presentation characterized by non-epileptic myoclonus and ataxia commencing in early infancy, abnormal opsoclonus-like eye movements, improvement of clinical symptoms under steroid treatment, and subsequent development of generalized epilepsy (PubMed:22638565).

Similarity:
Contains 1 BTB (POZ) domain.

Database links:

Entrez Gene: 417547 Chicken

Entrez Gene: 100124502 Cow

Entrez Gene: 154881 Human

Entrez Gene: 212919 Mouse

Entrez Gene: 688993 Rat

Omim: 611725 Human

SwissProt: Q5ZJP7 Chicken

SwissProt: A4IFB4 Cow

SwissProt: Q96MP8 Human

SwissProt: Q8BJK1 Mouse

SwissProt: B1WC97 Rat

Unigene: 546627 Human

Unigene: 55812 Mouse

Unigene: 103510 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.xucheq.com 北京博奧森生物技術(shù)有限公司
通過(guò)國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過(guò)國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
18VIDEOSEX性欧美69| EEUSS鲁丝片AV无码| 久久精品人妻一区二区三区| 驯服人妻HD中字日本| 大白肥妇BBVBBW高潮| 久久丫精品国产亚洲AV| 国产精品伦一区二区三级视频 | 亚洲精品久久久久久久观小说| 国产成人精品一区二三区| 国产超碰人人模人人爽人人添| 疯狂的交换小雅小姿1~6| 亚洲国产精品久久人人爱| 免费精品人在线二线三线区别| 免费人成在线观看网站体验站| 国产丰满老熟妇乱XXX1区| 亚洲AV无码片VR一区二区三区 | 99久久无码一区人妻A片| 尤物视频在线观看| 国产人妖乱国产精品人妖| 18一20亚洲gay无套| 国产又色又爽又刺激在线观看| 久久免费看少妇高潮A片| 日本猛少妇色XXXXX猛叫| 人妻被粗大猛进猛出国产| 久久99精品久久久久子伦| 最近免费中文字幕中文高清百度| 大肉大捧一进一出的视频| 国产又色又爽又刺激在线播放| 中文字幕精品一区二区精品 | 色窝窝无码一区二区三区| 国产午夜三级一区二区三| 无码AⅤ精品一区二区三区浪潮| 国产伦精品一区二区三区免费 | 亚洲国产精品尤物YW在线观看| 蜜桃传媒一区二区亚洲AV婷婷| 小荡货奶真大水多好紧视频| 公与淑婷厨房猛烈进出视频韩国 | 三妻四妾免费观看完整版高清| JAPANESEHD熟女熟妇伦| 99久久亚洲精品无码毛片| 朋友销魂的人妻|