吃奶呻吟打开双腿做受动态图 -亚洲色偷偷色噜噜狠狠99网-日韩精品极品视频在线观看免费-来一水AV@lysav

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  人才招聘  關(guān)于我們  聯(lián)系我們
13小男生GAY自慰脱裤子,精品国产一区二区三区AV性色,WWW国产精品内射老熟女
Rabbit Anti-TCTN3/BF647 Conjugated antibody (bs-12321R-BF647)
訂購(gòu)熱線:400-901-9800
訂購(gòu)郵箱:sales@xucheq.com
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@xucheq.com
說(shuō) 明 書(shū): 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-12321R-BF647
英文名稱1 Rabbit Anti-TCTN3/BF647 Conjugated antibody
中文名稱 BF647標(biāo)記的結(jié)構(gòu)蛋白家族3抗體
別    名 C10orf61; Chromosome 10 open reading frame 61; DKFZP564D116; TCTN3; TECT3_HUMAN; Tectonic 3; Tectonic 3 precursor; Tectonic family member 3; Tectonic-3; TECT3; UNQ1881/PRO4324; PSEC0041.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買        大包裝/詢價(jià)
說(shuō) 明 書(shū) 100ul  
研究領(lǐng)域 細(xì)胞生物  細(xì)胞凋亡  生長(zhǎng)因子和激素  
抗體來(lái)源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Chicken, Dog, Cow, Rabbit, Sheep, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 64kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human TCTN3/TECT3
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a member of the tectonic gene family which functions in Hedgehog signal transduction and development of the neural tube. Mutations in this gene have been associated with Orofaciodigital Syndrome IV and Joubert Syndrom 18. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Sep 2012].

Function:
Part of the tectonic-like complex which is required for tissue-specific ciliogenesis and may regulate ciliary membrane composition (By similarity). May be involved in apoptosis regulation. Necessary for signal transduction through the sonic hedgehog (Shh) signaling pathway

Subunit:
Part of the tectonic-like complex (also named B9 complex) (By similarity).

Subcellular Location:
Membrane; Single-pass type I membrane protein (Potential).

DISEASE:
Defects in TCTN3 are the cause of orofaciodigital syndrome 4 (OFD4) [MIM:258860]. A form of orofaciodigital syndrome, a group of heterogeneous disorders characterized by malformations of the oral cavity, face and digits, and associated phenotypic abnormalities that lead to the delineation of various subtypes. OFD4 patients have tongue nodules, multiple frenulae, broad flat nose, hypertelorism, and short rib polydactyly with tibial dysplasia (Majewski syndrome). The presence of severe tibial aplasia differentiates OFD4 from OFD1. Additional features of cystic dysplastic kidneys and brain malformation, including occipital encephalocele, are observed in severely affected patients.
Defects in TCTN3 are the cause of Joubert syndrome 18 (JBTS18) [MIM:614815]. A form of Joubert syndrome, a disorder presenting with cerebellar ataxia, oculomotor apraxia, hypotonia, neonatal breathing abnormalities and psychomotor delay. Neuroradiologically, it is characterized by cerebellar vermian hypoplasia/aplasia, thickened and reoriented superior cerebellar peduncles, and an abnormally large interpeduncular fossa, giving the appearance of a molar tooth on transaxial slices (molar tooth sign). Additional variable features include retinal dystrophy and renal disease. JBTS18 patients have vermis agenesis and the molar tooth sign as well as severe kyphoscoliosis. Other features include intrauterine growth retardation, oral anomalies, micrognathism, polydactyly and camptodactyly, joint laxity, horseshoe kidney, and ventricular septal defect. Note=TCTN3-mutated fibroblasts from JBTS18 patients fail to respond to Shh agonists suggesting that at least some of the defects in affected individuals may be secondary to reduced Shh signaling (PubMed:22883145).

Similarity:
Belongs to the tectonic family.

Database links:

Entrez Gene: 26123 Human

Entrez Gene: 67590 Mouse

Entrez Gene: 309486 Rat

SwissProt: Q6NUS6 Human

SwissProt: Q8R2Q6 Mouse

Unigene: 438991 Human

Unigene: 374056 Mouse

Unigene: 60758 Mouse



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.xucheq.com 北京博奧森生物技術(shù)有限公司
通過(guò)國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書(shū)編號(hào): 00124Q34771R2M/1100
通過(guò)國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書(shū)編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
特黄a级毛片免费视频| 99久久精品毛片免费播放高潮| 精品国产污污免费网站入口| 美女视频黄是免费| 亚洲 欧美 激情 小说 另类| 最近中文字幕在线看免费完整版 | 久久99国产精一区二区三区| 无码国产精品一区二区免费式直播 | 一个人看的www免费视频| 久久久久亚洲精品中文字幕| ASS白嫩白嫩的少妇PICS| 久久久久亚洲AV成人网人人软件 | 中文字幕精品久久久久人妻| 国产精品日日做人人爱| 欧美最猛黑人XXXXX猛交| 精品无码三级在线观看视频| 无码人妻一区二区三区精品视频 | 影音先锋女人AV鲁色资源网久久 | 性欧美xxxxx乱极品少妇| 国产精品久久久久久人妻精品| 顶级少妇倣爱A片XXX| 久久久久噜噜噜亚洲熟女综合| 秋霞电影网| 亚洲AV无码一区二区三区观看| 亚洲中文字幕无码爆乳AV久久| 97精品超碰一区二区三区| 夜里十大禁用直播APP| 免费看国产曰批40分钟| 国产精品久久久久AAAA| 亚洲成av人片一区二区密柚| 亚洲AV综合色区无码一二三区| 无码日本精品XXXXXXXXX| 亚洲人精品午夜射精日韩| 极品少妇高潮啪啪AV无码| 天天躁日日躁AAAAXXXX| 国产精品久久久久AAAA| 无码少妇高潮浪潮AV久久| 国产精品视频在线观看| 巨大黑人极品VIDEOS精品| 狠狠做深爱婷婷久久综合一区| 国产成人亚洲精品|