吃奶呻吟打开双腿做受动态图 -亚洲色偷偷色噜噜狠狠99网-日韩精品极品视频在线观看免费-来一水AV@lysav

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  人才招聘  關(guān)于我們  聯(lián)系我們
久久夜色精品国产噜噜亚洲av ,少妇高潮抽搐无码AV久久
Rabbit Anti-MCFD2/PE-Cy3 Conjugated antibody (bs-24080R-PE-Cy3)
訂購(gòu)熱線:400-901-9800
訂購(gòu)郵箱:sales@xucheq.com
訂購(gòu)QQ:  400-901-9800
技術(shù)支持:techsupport@xucheq.com
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-24080R-PE-Cy3
英文名稱1 Rabbit Anti-MCFD2/PE-Cy3 Conjugated antibody
中文名稱 PE-Cy3標(biāo)記的多種凝血因子缺乏蛋白2抗體
別    名 1810021C21Rik; DKFZp686G21263; F5F8D; LMAN1IP; MCFD 2; Mcfd2; MCFD2_MOUSE; Multiple coagulation factor deficiency protein 2; Neural stem cell derived neuronal survival protein; Neural stem cell-derived neuronal survival protein; SDNSF.  
規(guī)格價(jià)格 100ul/2980元 購(gòu)買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  神經(jīng)生物學(xué)  信號(hào)轉(zhuǎn)導(dǎo)  干細(xì)胞  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) Mouse, Rat, 
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 16kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from mouse MCFD2
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.05M PB, pH 7.5.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a soluble luminal protein with two calmodulin-like EF-hand motifs at its C-terminus. This protein forms a complex with LAMN1 (lectin mannose binding protein 1; also known as ERGIC-53) that facilitates the transport of coagulation factors V (FV) and VIII (FVIII) from the endoplasmic reticulum to the Golgi apparatus via an endoplasmic reticulum Golgi intermediate compartment (ERGIC). Mutations in this gene cause combined deficiency of FV and FVIII (F5F8D); a rare autosomal recessive bleeding disorder characterized by mild to moderate bleeding and coordinate reduction in plasma FV and FVIII levels. This protein has also been shown to maintain stem cell potential in adult central nervous system and is a marker for testicular germ cell tumors. The 3' UTR of this gene contains a transposon-like human repeat element named 'THE 1'. A processed RNA pseudogene of this gene is on chromosome 6p22.1. Alternative splicing results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, Jun 2010]

Function:
The MCFD2-LMAN1 complex forms a specific cargo receptor for the ER-to-Golgi transport of selected proteins. Plays a role in the secretion of coagulation factors.

Subcellular Location:
Endoplasmic reticulum-Golgi intermediate compartment; Endoplasmic reticulum; Golgi apparatus;

DISEASE:
Defects in MCFD2 are a cause of factor V and factor VIII combined deficiency type 2 (F5F8D2) [MIM:613625]; also known as multiple coagulation factor deficiency 2 (MCFD2). F5F8D2 is a blood coagulation disorder characterized by bleeding symptoms similar to those in hemophilia or parahemophilia, that are caused by single deficiency of FV or FVIII, respectively. The most common symptoms are epistaxis, menorrhagia, and excessive bleeding during or after trauma. Plasma levels of coagulation factors V and VIII are in the range of 5 to 30% of normal.

Similarity:
Contains 2 EF-hand domains.

Database links:

Entrez Gene: 90411 Human

Entrez Gene: 193813 Mouse

Omim: 607788 Human

SwissProt: Q8NI22 Human

SwissProt: Q8K5B2 Mouse

Unigene: 293689 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.xucheq.com 北京博奧森生物技術(shù)有限公司
通過國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
色欲人妻综合AAAAAAAA网| 久久久久久AV无码免费看大片| 亚洲精品久久久久AV无码| 天天操,天天干,天天日| 玩弄白嫩少妇XXXXX性| 久久久GOGO无码啪啪艺术 | 国产精品美女久久久免费| 少妇高潮一区二区三区99 | 天天狠天天透天干天天怕∴| 中文字幕日韩一区二区三区不卡| XX性欧美肥妇精品久久久久久| 成人无码精品1区2区3区免费看| 国产精品宅男擼66M3U8| 欧美成人片一区二区三区| 国产伦孑沙发午休精品| 夜夜爽www| 哦┅┅快┅┅用力啊┅警花少妇 | 麻豆传煤入口免费进入2023| 国产免费AV片无码永久免费| 草色噜噜噜AV在线观看香蕉| 亚洲日韩一区二区三区| 国产午夜片无码区在线播放| 成人AAA片一区国产精品| 国产精品爽黄69天堂A片潘金莲| 国产伦精品一区二区三区妓女 | 国产欧美一区二区精品久久久 | 欧美亚洲色综久久精品国产| 国产欧美精品区一区二区三区 | 久久亚洲AV午夜福利精品一区| 人妻无码αv中文字幕久久琪琪布| 一本色道无码道DVD在线观看| 精品人人妻人人澡人人爽牛牛 | 亚洲av午夜精品一区二区三区| 小婕子的第一次好紧| 欧美熟妇VIVOE精品| 精品乱人伦一区二区三区| 三级黄色视频| 精品午夜福利在线观看| 三年片在线观看免费大全爱奇艺| 日韩精品一区二区亚洲AV观看 | 久久中文字幕人妻熟AV女|