吃奶呻吟打开双腿做受动态图 -亚洲色偷偷色噜噜狠狠99网-日韩精品极品视频在线观看免费-来一水AV@lysav

掃碼關(guān)注公眾號           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  人才招聘  關(guān)于我們  聯(lián)系我們
色一情一区二,国产乱码一区二区三区,男人添女人下部高潮全视频
Rabbit Anti-MCFD2/BF594 Conjugated antibody (bs-24080R-BF594)
訂購熱線:400-901-9800
訂購郵箱:sales@xucheq.com
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@xucheq.com
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產(chǎn)品編號 bs-24080R-BF594
英文名稱1 Rabbit Anti-MCFD2/BF594 Conjugated antibody
中文名稱 BF594標(biāo)記的多種凝血因子缺乏蛋白2抗體
別    名 1810021C21Rik; DKFZp686G21263; F5F8D; LMAN1IP; MCFD 2; Mcfd2; MCFD2_MOUSE; Multiple coagulation factor deficiency protein 2; Neural stem cell derived neuronal survival protein; Neural stem cell-derived neuronal survival protein; SDNSF.  
規(guī)格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領(lǐng)域 細胞生物  神經(jīng)生物學(xué)  信號轉(zhuǎn)導(dǎo)  干細胞  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) Mouse, Rat, 
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 16kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from mouse MCFD2
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
This gene encodes a soluble luminal protein with two calmodulin-like EF-hand motifs at its C-terminus. This protein forms a complex with LAMN1 (lectin mannose binding protein 1; also known as ERGIC-53) that facilitates the transport of coagulation factors V (FV) and VIII (FVIII) from the endoplasmic reticulum to the Golgi apparatus via an endoplasmic reticulum Golgi intermediate compartment (ERGIC). Mutations in this gene cause combined deficiency of FV and FVIII (F5F8D); a rare autosomal recessive bleeding disorder characterized by mild to moderate bleeding and coordinate reduction in plasma FV and FVIII levels. This protein has also been shown to maintain stem cell potential in adult central nervous system and is a marker for testicular germ cell tumors. The 3' UTR of this gene contains a transposon-like human repeat element named 'THE 1'. A processed RNA pseudogene of this gene is on chromosome 6p22.1. Alternative splicing results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, Jun 2010]

Function:
The MCFD2-LMAN1 complex forms a specific cargo receptor for the ER-to-Golgi transport of selected proteins. Plays a role in the secretion of coagulation factors.

Subcellular Location:
Endoplasmic reticulum-Golgi intermediate compartment; Endoplasmic reticulum; Golgi apparatus;

DISEASE:
Defects in MCFD2 are a cause of factor V and factor VIII combined deficiency type 2 (F5F8D2) [MIM:613625]; also known as multiple coagulation factor deficiency 2 (MCFD2). F5F8D2 is a blood coagulation disorder characterized by bleeding symptoms similar to those in hemophilia or parahemophilia, that are caused by single deficiency of FV or FVIII, respectively. The most common symptoms are epistaxis, menorrhagia, and excessive bleeding during or after trauma. Plasma levels of coagulation factors V and VIII are in the range of 5 to 30% of normal.

Similarity:
Contains 2 EF-hand domains.

Database links:

Entrez Gene: 90411 Human

Entrez Gene: 193813 Mouse

Omim: 607788 Human

SwissProt: Q8NI22 Human

SwissProt: Q8K5B2 Mouse

Unigene: 293689 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.xucheq.com 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號: 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號: CQC24QY10047R0M/1100
京ICP備05066980號-1         京公網(wǎng)安備110107000727號
国产成人精品三级麻豆| B站禁止转播404入口| 亚洲日韩乱码久久久久久| 无码GOGO大胆啪啪艺术| 99蜜桃臀久久久欧美精品网站 | WWW国产精品内射老熟女| 久久人妻内射无码一区三区| 久久精品无码一区二区日韩av| 亚洲欧美一区二区三区| 久久精品国产亚洲av高清热| 亚洲AV无码国产精品久久不卡| 亚洲乱码国产乱码精品精| 少妇高潮一区二区三区99| 精品久久人妻AV中文字幕| 国产精品99久久久久久WWW| 人妻精品久久久久中文字幕| 国产无遮挡又黄又爽在线观看| 亚洲精品久久久久久一区二区| 免费人成在线观看网站体验站 | 亚洲AV毛片一区二区三区| 老熟妇仑乱视频一区二区| 精品人人妻人人澡人人爽牛牛| 成人AAA片一区国产精品| 狠狠做深爱婷婷久久综合一区| 亚洲AV无码精品色午夜果冻不卡| 国产人妻精品无码AV在线五十路| 校花不着寸缕的跪趴在地下视频| 亚洲AV久久无码| 天堂а√在线中文在线| 波多野结衣电影| 欧美性xxxxx极品少妇| 免费无码国产V片在线观看| 免费A级毛片做爰片在线| 国产成人无码AA精品一区| 亚洲VA欧美VA天堂V国产综合 | 欧美交换国产一区内射| 国产初高中精品无码专区| 亚洲AV无码一区二区二三区| WWW夜插内射视频网站| 亚洲AV无码久久| 丰满人妻在公车被猛烈进入电影|